Abstract Unicuspid aortic valve (UAV) is a rare congenital anomaly, frequently associated with early progression to severe aortic stenosis and aortopathy. We report the case of a 38-year-old woman who presented with difficult-to-control hypertension and progressive exertional dyspnea. Transthoracic echocardiography revealed critical aortic stenosis (peak gradient of 183 mmHg, mean gradient of 125 mmHg, and valve area of 0.59 cm2), associated with mild aortic regurgitation and ascending aortic dilation (45–46 mm). Three-dimensional transesophageal echocardiography confirmed a unicommissural UAV, as well […]

Introduction The prevalence of anomalous chordae in the aortic valve is rare in clinical practice. These anomalies, although uncommon, can have significant clinical implications, including valve insufficiency, arrhythmias and/or embolic risk. Accurate diagnosis and understanding of its pathophysiology are essential for adequate patient management. The uncommon nature of anomalous chordae in the aortic valve means that their presence can often go unnoticed or misdiagnosed. Medical literature presents few reports on these structures of probable embryonic origin, leaving gaps in clinical […]