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A publication of the Cardiovascular Imaging Department of the Brazilian Society of Cardiology
Uma publicação do Departamento de Imagem Cardiovascular da Sociedade Brasileira de Cardiologia
DOI: 10.36660/abcimg.20260038i
Introduction Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis constitute a group of systemic small-vessel inflammatory diseases characterized by pauci-immune necrotizing vasculitis and multisystem involvement, including granulomatosis with polyangiitis (GPA), eosinophilic granulomatosis with polyangiitis (EGPA), and microscopic polyangiitis (MPA).– MPA is classically associated with rapidly progressive glomerulonephritis and alveolar hemorrhage, conditions that carry high morbidity and mortality when not promptly recognized and treated., In addition to predominant renal and pulmonary involvement, there is growing evidence that patients with ANCA-associated vasculitis have an increased […]
Keywords: Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis; Dilated Cardiomyopathy; Echocardiography; Microscopic Polyangiitis