Sarcoidosis is a systemic granulomatous disorder of unknown cause that can affect virtually any organ. The extracardiac forms are usually benign and subjected to spontaneous remission. However, the prognosis may be unfavorable in case of cardiac involvement.
Symptomatic cardiac sarcoidosis (CS) is diagnosed in approximately 5% of patients with sarcoidosis. However, based on some autopsy series, the prevalence of subclinical CS can reach 25–30%.
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Cardiac Sarcoidosis as a Cause of Total Atrioventricular Block: Importance of Differential Diagnosis
Elias NetoJ, SilvaMA, KuniyoshiRR, FuturoG, MerçonES, GrativvolPS, PedrottiFC. Cardiac Sarcoidosis as a Cause of Total Atrioventricular Block: Importance of Differential Diagnosis. Arq Bras Cardiol: Imagem cardiovasc. 2021;34(1):eabc163.
Elias Neto,Jorge; Silva,Márcio Augusto; Kuniyoshi,Ricardo Ryoshim; Futuro,Guilherme; Merçon,Erick Sessa; Grativvol,Petherson Susano; Pedrotti,Fátima Cristina. Cardiac Sarcoidosis as a Cause of Total Atrioventricular Block: Importance of Differential Diagnosis. Arq Bras Cardiol: Imagem cardiovasc., v. 34, n. 1, eabc163, Mar. 2021.
Elias Neto,J., Silva,M.A., Kuniyoshi,R.R., Futuro,G., Merçon,E.S., Grativvol,P.S., & Pedrotti,F.C. (2021). Cardiac Sarcoidosis as a Cause of Total Atrioventricular Block: Importance of Differential Diagnosis. Arq Bras Cardiol: Imagem cardiovasc.,34(1), eabc163.
Elias Neto,Jorge and Silva,Márcio Augusto and Kuniyoshi,Ricardo Ryoshim and Futuro,Guilherme and Merçon,Erick Sessa and Grativvol,Petherson Susano and Pedrotti,Fátima Cristina. Cardiac Sarcoidosis as a Cause of Total Atrioventricular Block: Importance of Differential Diagnosis. Arq Bras Cardiol: Imagem cardiovasc. [online]. 2021, vol. 34, n. 1, [cited 2026-03-06], eabc163. Available from: <https://www.abcimaging.org/article/cardiac-sarcoidosis-as-a-cause-of-total-atrioventricular-block-importance-of-differential-diagnosis/>. ISSN .
Figure 1
(A) Complete atrioventricular block. (B) Telemetry record of the device showing an episode of ventricular tachycardia (approximately 300 ms/200 bpm cycle) with effective therapy.