Abstract Mitral valve malformations are considered rare even in their association with other anomalies, except for mitral valve prolapse, which is found in approximately 10% of the population. Mitral valve abnormalities may affect any portion of the valve or subvalvular apparatus (annulus, cusp, tendinous cords or papillary muscles).1,2 Mitral valve anatomy and function can be assessed by echocardiography, resonance or cardiac tomography, and is essential for potential therapeutic programming.2